Idiopathic Pulmonary Fibrosis: A Systemic Disease?
نویسندگان
چکیده
introDuCtion Idiopathic pulmonary fibrosis (IPF) is a specific type of chronic progressive fibrosing interstitial pneumonia associated with a histopathologic pattern of usual interstitial pneumonia. IPF is typically considered to be a lung‐limited disorder. Although the primary manifestations of IPF are pulmonary in nature, IPF is increasingly recognized as a systemic disease due to its strong association with comorbidities and complications.
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